Published May 1997
| Version v1
Journal article
Non-marfan idiopathic medionecrosis (cystic medial necrosis) presenting with multiple visceral artery aneurysms and diffuse connective tissue fragility: Two brothers
Creators
- 1. Gunma University School of Medicine, Department of Nuclear Medicine (Japan)
- 2. Gunma University School of Medicine, Department of Diagnostic Radiology (Japan)
- 3. Gunma University School of Medicine, Department of Hygiene and Virology (Japan)
- 4. Gunma University School of Medicine, Department of Second Surgery (Japan)
- 5. Gunma Health Foundation (Japan)
Description
Two brothers with multiple visceral artery aneurysms or dilatations and diffuse connective tissue fragility who did not have clinical features of Marfan syndrome are reported. One presented with retroperitoneal hemorrhage during angiography, and idiopathic medionecrosis was proved by resection of the aneurysms. These cases belong to the heterogeneous group of Marfan syndrome. The angiographical features (multiple dilation of visceral arteries) suggests fragility of connective tissue and is predictive of hazards during and after a catheterization and operation
Additional details
Identifiers
Publishing Information
- Journal Title
- Cardiovascular and Interventional Radiology
- Journal Volume
- 20
- Journal Issue
- 3
- Journal Page Range
- p. 225-227
- ISSN
- 0174-1551
- CODEN
- CAIRDG
INIS
- Country of Publication
- United States
- Country of Input or Organization
- International Atomic Energy Agency (IAEA)
- INIS RN
- 39092879
- Subject category
- S62: RADIOLOGY AND NUCLEAR MEDICINE;
- Descriptors DEI
- ARTERIES; BIOMEDICAL RADIOGRAPHY; CONNECTIVE TISSUE; HEMORRHAGE; NECROSIS
- Descriptors DEC
- ANIMAL TISSUES; BLOOD VESSELS; BODY; CARDIOVASCULAR SYSTEM; DIAGNOSTIC TECHNIQUES; MEDICINE; NUCLEAR MEDICINE; ORGANS; PATHOLOGICAL CHANGES; RADIOLOGY; SYMPTOMS
Optional Information
- Copyright
- Copyright (c) 1997 Springer-Verlag New York Inc