Published May 1, 2015 | Version v1
Journal article

Conservative management of a perianal rhabdomyosarcoma in a 2-year old child by Papillon's technique

  • 1. Faculty of Medicine, University of Nantes, Nantes (France)
  • 2. Department of Radiotherapy, Institut de Cancérologie de l'Ouest- René Gauducheau, Bd J Monod, 44800 Nantes, St-Herblain (France)
  • 3. Department of Pediatric Oncology, Institut Gustave Roussy, 39, rue Camille Desmoulins, 94805 Villejuif (France)
  • 4. Department of Brachytherapy, Institut Gustave Roussy, 39, rue Camille Desmoulins, 94805 Villejuif (France)
  • 5. Department of Pediatric Oncology, Centre Hospitalier Universitaire, Place Ricordeau, Nantes (France)

Description

Rhabdomyosarcoma (RMS) is the most common sarcoma in paediatric patients. A perianal site is unusual and is associated with a low cure rate. The few cases of reported perianal RMS have been associated with sequelae. Here, we report the case of a 29-month-old male child who received sequential treatment by surgery, chemotherapy and radiotherapy inspired by Papillon's irradiation of adult anal/low-rectum cancers (including external beam radiotherapy in the gynecological exam position followed by brachytherapy) and who remains in complete remission 49 months post treatment with no sphincter or other anorectal disorders

Availability note (English)

Available from http://dx.doi.org/10.1186/s13014-015-0413-9; Available from http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4422314

Additional details

Publishing Information

Journal Title
Radiation Oncology (Online)
Journal Volume
10
Journal Page Range
vp.
ISSN
1748-717X

INIS

Country of Publication
United Kingdom
Country of Input or Organization
International Atomic Energy Agency (IAEA)
INIS RN
47069974
Subject category
S62: RADIOLOGY AND NUCLEAR MEDICINE;
Descriptors DEI
BRACHYTHERAPY; CHEMOTHERAPY; CHILDREN; CONNECTIVE TISSUE; EXTERNAL BEAM RADIATION THERAPY; SARCOMAS
Descriptors DEC
AGE GROUPS; ANIMAL TISSUES; ANIMALS; BODY; DISEASES; MAMMALS; MAN; MEDICINE; NEOPLASMS; NUCLEAR MEDICINE; PRIMATES; RADIOLOGY; RADIOTHERAPY; THERAPY; VERTEBRATES

Optional Information

Copyright
Copyright (c) Demoor-Goldschmidt et al.
Notes
PMCID: PMC4422314; PMID: 25927819; PUBLISHER-ID: 413; OAI: oai:pubmedcentral.nih.gov:4422314; licensee BioMed Central. 2015