Published June 1988
| Version v1
Journal article
Pippow's syndrome
Creators
Description
For the first time since the initial report of aplasia of vertebral joints and brachydactyly occurring in a sibship, a similar family history of this rare dystostosis is presented. The following triad of symptoms is significant: a) Hypoplasia of the laminae and of the articular and transverse processes of the vertebrae in the thoracolumbar region; b) cranial shift of the vertebral junctions; and c) brachydactyly. 'Pippow's syndrome' and 'Pippow's dysostosis' are suggested as possible names for this condition. (orig.)
Abstract (German)
Erstmals nach der Beschreibung von 'Wirbelgelenkaplasien und Brachydaktylie in einer Sippe' durch G. Pippow wird ueber eine gleichartige Kasuistik berichtet. Es ergibt sich folgende charakteristische Symptomentrias: a) Hypoplasie von Lamina, Gelenk- und Querfortsaetzen von Wirbeln des thorako-lumbalen Ueberganges; b) Kranialvariation der Wirbelsaeulenuebergaenge und c) Brachydaktylie. Einem Vorschlag von A. Wackenheim folgend werden die Bezeichnungen Pippow-Syndrom oder Pippow's Dysostose vorgeschlagen. (orig.)Additional details
Additional titles
- Original title (German)
- Ueber das Pippow-Syndrom
Publishing Information
- Journal Title
- Radiologe
- Journal Volume
- 28
- Journal Issue
- 6
- Series
- Radiologe.
- Journal Page Range
- 289-293
- ISSN
- 0033-832X
- CODEN
- RDLGB
INIS
- Country of Publication
- Germany
- Country of Input or Organization
- Germany
- INIS RN
- 19072391
- Subject category
- S62: RADIOLOGY AND NUCLEAR MEDICINE;
- Descriptors DEI
- BIOMEDICAL RADIOGRAPHY; CHEST; CONGENITAL MALFORMATIONS; DIAGNOSIS; HANDS; HEREDITARY DISEASES; IMAGES; PATIENTS; SKELETAL DISEASES; SKELETON; X-RAY RADIOGRAPHY
- Descriptors DEC
- ARMS; BODY; BODY AREAS; DIAGNOSTIC TECHNIQUES; DISEASES; LIMBS; MALFORMATIONS; MEDICINE; ORGANS; PATHOLOGICAL CHANGES