Infra hepatic interruption of inferior vena cava

Congenital anomaly of IVC is rare, but understanding of this anomaly is important in radiological diagnosis angiographic procedures and major retroperitoneal and thoracic surgery. We analysed 23 cases of IVC interruption diagnosed by cardiac angiography at Seoul National University Hospital. The results were as follows: 1. The incidence of intrahepatic interruption of IVC was 0.45% of the patients having cardiac angiography and most patients showed cyanosis (91%). 2. The most common associated cardiac anomaly was right ventricular outflow tract obstruction (60%). Other associated cardiac defects were VSD, ASD, valvular anomalies in 9 cases (39%) respectively; double outlet right ventricle, bilateral superior vena cava, single ventricle in 6 cases (26%) respectively; single atrium, PDA in 5 cases (22%) respectively. 6 cases of situs inverses, 3 cases if sutus ambiguous, 2 cases of visceral heterotaxia and one case of asplenia were observed also. 7 cases of left-sided IVC were associated with IVC interruption in normal situs.