Published May 1985 | Version v1
Journal article

Narrow trachea in mucopolysaccharidoses

  • 1. Wisconsin Univ., Madison (USA). Clinical Science Center

Description

Nine of 56 patients with mucopolysaccharidosis (MPS) showed small tracheal diamters on the frontal chest radiographs. Autopsy of an MPS I-H (Hurler disease) patient demonstrated that the small calibre was secondary to deposition of glycosaminoglycan (mucopolysaccharide). Autopsies of two patients with other storage diseases, one with geleophysic dysplasia and one with mucolipidosis II, also exhibited compromise of their airways because of storage material accumulation. (orig.)

Additional details

Publishing Information

Journal Title
Pediatr. Radiol.
Journal Volume
15
Journal Issue
4
Series
CODEN: PDRYA.;Pediatr. Radiol.
Journal Page Range
225-228
ISSN
0301-0449

Conference

Title
20. annual congress of the European Society of Paediatric Radiology.
Dates
2-7 May 1983.
Place
Paris (France).

INIS

Country of Publication
Germany
Country of Input or Organization
Germany
INIS RN
16054108
Subject category
S62: RADIOLOGY AND NUCLEAR MEDICINE;
Resource subtype / Literary indicator
Conference
Descriptors DEI
BIOMEDICAL RADIOGRAPHY; DIAGNOSIS; IMAGES; METABOLIC DISEASES; MUCOPOLYSACCHARIDES; PATHOLOGICAL CHANGES; PATIENTS; SYMPTOMS; TRACHEA; X-RAY RADIOGRAPHY
Descriptors DEC
AMINES; CARBOHYDRATES; DIAGNOSTIC TECHNIQUES; DISEASES; MEDICINE; ORGANIC COMPOUNDS; POLYSACCHARIDES; RESPIRATORY SYSTEM; SACCHARIDES