Published May 1985
| Version v1
Journal article
Narrow trachea in mucopolysaccharidoses
- 1. Wisconsin Univ., Madison (USA). Clinical Science Center
Description
Nine of 56 patients with mucopolysaccharidosis (MPS) showed small tracheal diamters on the frontal chest radiographs. Autopsy of an MPS I-H (Hurler disease) patient demonstrated that the small calibre was secondary to deposition of glycosaminoglycan (mucopolysaccharide). Autopsies of two patients with other storage diseases, one with geleophysic dysplasia and one with mucolipidosis II, also exhibited compromise of their airways because of storage material accumulation. (orig.)
Additional details
Publishing Information
- Journal Title
- Pediatr. Radiol.
- Journal Volume
- 15
- Journal Issue
- 4
- Series
- CODEN: PDRYA.;Pediatr. Radiol.
- Journal Page Range
- 225-228
- ISSN
- 0301-0449
Conference
- Title
- 20. annual congress of the European Society of Paediatric Radiology.
- Dates
- 2-7 May 1983.
- Place
- Paris (France).
INIS
- Country of Publication
- Germany
- Country of Input or Organization
- Germany
- INIS RN
- 16054108
- Subject category
- S62: RADIOLOGY AND NUCLEAR MEDICINE;
- Resource subtype / Literary indicator
- Conference
- Descriptors DEI
- BIOMEDICAL RADIOGRAPHY; DIAGNOSIS; IMAGES; METABOLIC DISEASES; MUCOPOLYSACCHARIDES; PATHOLOGICAL CHANGES; PATIENTS; SYMPTOMS; TRACHEA; X-RAY RADIOGRAPHY
- Descriptors DEC
- AMINES; CARBOHYDRATES; DIAGNOSTIC TECHNIQUES; DISEASES; MEDICINE; ORGANIC COMPOUNDS; POLYSACCHARIDES; RESPIRATORY SYSTEM; SACCHARIDES