Published 2013 | Version v1
Journal article

Adams Oliver syndrome: Description of a new phenotype with cerebellar abnormalities in a family

  • 1. Department of Advanced Biomedical Sciences, Unit of Neuroradiology, Federico II University, Naples (Italy)
  • 2. Department of Translational Medical Sciences, Section of Pediatrics, Federico II University, Naples (Italy)

Description

To describe cerebellar abnormalities in a family composed by a father and two affected sibs with Adams Oliver syndrome (AOS) (OMIM 100300). Brain MRI and MR angiography were performed at 1.5T. The siblings presented cerebellar cortex dysplasia characterized by the presence of cysts. Abnormalities of CNS are an unusual manifestation of AOS. To our knowledge, this is the first report of cerebellar cortical dysplasia in a family with AOS

Availability note (English)

Available from http://dx.doi.org/10.12659/PJR.889531; Available from http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3908514

Additional details

Publishing Information

Journal Title
Polish Journal of Radiology
Journal Volume
78
Journal Issue
4
Journal Page Range
p. 83-87
ISSN
1733-134X

INIS

Country of Publication
Poland
Country of Input or Organization
International Atomic Energy Agency (IAEA)
INIS RN
47031355
Subject category
S62: RADIOLOGY AND NUCLEAR MEDICINE;
Descriptors DEI
BIOMEDICAL RADIOGRAPHY; BLOOD VESSELS; CYSTS; NMR IMAGING; PHENOTYPE
Descriptors DEC
BODY; CARDIOVASCULAR SYSTEM; DIAGNOSTIC TECHNIQUES; MEDICINE; NUCLEAR MEDICINE; ORGANS; PATHOLOGICAL CHANGES; RADIOLOGY

Optional Information

Copyright
Copyright (c) Pol J Radiol, 2013
Notes
PMCID: PMC3908514; PMID: 24505229; PUBLISHER-ID: poljradiol-78-4-83; OAI: oai:pubmedcentral.nih.gov:3908514; This is an open access article. Unrestricted non-commercial use is permitted provided the original work is properly cited.