Rhomboencephalosynapsis: A Case Report

Rhomboencephalosynapsis is an uncommon congenital malformation of the posterior fossa, that consists of agenesia of the vermis and fusion of cerebellar hemispheres in the middle line. It is usually associated with supratentorial alterations like hidrocephaly and thalamic fusion,that condition the prognosis of the patient. We describe the case of a 10 month patient with rhomboencephalosynapsis.