Published February 1998 | Version v1
Journal article

Osteogenesis imperfecta with joint contractures: Bruck syndrome

  • 1. Department of Radiology, University of Medicine and Dentistry of New Jersey, 150 Bergen St., Rm. C320, Newark, NJ 07103-2426 (United States)
  • 2. Center for Human and Molecular Genetics, Department of Pediatrics, University of Medicine and Dentistry of New Jersey, Newark, New Jersey (United States)
  • 3. Department of Radiology, Newark-Beth Israel Medical Center, Newark, New Jersey (United States)

Description

We describe an Egyptian boy with osteogenesis imperfecta who was born with thumb contractures and bilateral antecubital pterygia. He was seen at 16 months of age with femur and tibial fractures, thoracic vertebral compression fractures, scoliosis and Wormian bones. The findings are consistent with a diagnosis of Bruck syndrome. (orig.)

Additional details

Publishing Information

Journal Title
Pediatric Radiology
Journal Volume
28
Journal Issue
2
Journal Page Range
p. 117-119.
ISSN
0301-0449
CODEN
PDRYA5

INIS

Country of Publication
Germany
Country of Input or Organization
Germany
INIS RN
29022455
Subject category
S62: RADIOLOGY AND NUCLEAR MEDICINE;
Descriptors DEI
CHEST; EGYPTIAN ARAB REPUBLIC; FEMUR; FRACTURES; IMAGES; MALFORMATIONS; NEONATES; PATHOLOGICAL CHANGES; SKELETON; TIBIA; VERTEBRAE
Descriptors DEC
AFRICA; ANIMALS; ARAB COUNTRIES; BODY; BODY AREAS; DEVELOPING COUNTRIES; DISEASES; FAILURES; MIDDLE EAST; ORGANS

Optional Information

Notes
With 1 fig., 5 refs.